Laparoscopic Hemi-hysterectomy and Trachelectomy in a Case of Herlyn-Werner-Wunderlich Syndrome

Abstract:

Background: Herlyn-Werner-Wunderlich Syndrome (HWWS) is a rare Müllerian anomaly characterized by uterus didelphys coexisting with an obstructed hemivagina and ipsilateral renal agenesis. Case: A 13-year-old female presented one-year after menarche with severe dysmenorrhea and a right-sided pelvic mass. Imaging identified a right uterus with hematometra, hematocolpos, absent right kidney, normal left kidney, ureter, left uterus, and vagina compressed to the left by right hematocolpos. We performed laparoscopic hemi-hysterectomy of the non-communicating hemi-uterus, and laparoscopic trachelectomy. Conclusion: Laparoscopic hemi-hysterectomy and trachelecotmy is a minimally invasive surgical option for patients with Herlyn-Werner-Wunderlich Syndrome.

Authors:

Entidhar Al Sawah, MD, Obstetrics and Gynecology Resident, Shayne M. Plosker, MD, Professor and Chief, Division of Reproductive Endocrinology and Infertility, Emad Mikhail MBChB, MD, FACOG, Assistant Professor, Minimally Invasive Gynecologic, Surgeon, Department of Obstetrics and Gynecology, University of South Florida Morsani College of Medicine, Tampa, Florida

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